Anaesthetic management of an obstetric patient with Pompe disease.

Abstract:

:Pompe disease (Glycogen storage disease type II) leads to abnormal glycogen deposition in various vital organs resulting in multiple systemic sequelae. We present the anaesthetic management for caesarean section of a 31-year-old parturient with known Pompe disease. The parturient had symptoms and signs of respiratory dysfunction and the pregnancy was complicated by preeclampsia. She underwent urgent caesarean section under regional anaesthesia resulting in the birth of a healthy baby girl. To our knowledge, this is the first reported case of both spinal anaesthesia for caesarean section and successful live birth in a patient with Pompe disease.

journal_name

Int J Obstet Anesth

authors

Cilliers HJ,Yeo ST,Salmon NP

doi

10.1016/j.ijoa.2007.11.001

subject

Has Abstract

pub_date

2008-04-01 00:00:00

pages

170-3

issue

2

eissn

0959-289X

issn

1532-3374

pii

S0959-289X(07)00181-1

journal_volume

17

pub_type

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