[Possible etiologies of West syndrome: evaluation of 95 patients].

Abstract:

OBJECTIVE:To describe the etiologies of West syndrome (WS) among children followed in a rehabilitation center. METHOD:Retrospective study with emphasis in the following items: gender, age at the diagnosis of WS and its etiology. The etiologies were divided into three categories: symptomatic, cryptogenic and idiopathic. Symptomatic cases were classified as follows: pre, post and perinatal. RESULTS:Ninety-five patients were included. Fifty-nine were boys (62%). Mean age at the diagnosis was 4.9 (+/- 5.0) months. There were 25 cryptogenic (26.3%), one idiopathic (1.1%) and 69 (72.6%) symptomatic cases, most of them of perinatal origin. CONCLUSION:Our findings are in agreement with the literature. In the future, as our knowledge in the field of WS and its diagnostic methods increase, there will be a small number of cryptogenic and idiopathic cases.

journal_name

Arq Neuropsiquiatr

authors

Matta AP,Chiacchio SV,Leyser M

doi

10.1590/s0004-282x2007000400022

subject

Has Abstract

pub_date

2007-09-01 00:00:00

pages

659-62

issue

3A

eissn

0004-282X

issn

1678-4227

pii

S0004-282X2007000400022

journal_volume

65

pub_type

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