Idiopathic short QT interval: a new clinical syndrome?

Abstract:

:In this first clinical report of an idiopathic familial persistently short QT interval (QTI), we describe three members of one family (a 17-year-old female, her 21-year-old brother, and their 51-year-old mother) demonstrating this ECG phenomenon, associated in the 17-year-old with several episodes of paroxysmal atrial fibrillation requiring electrical cardioversion. Similar ECG changes seen in an unrelated 37-year-old patient were associated with sudden cardiac death. Our report also describes other manifestations of abnormal shortening of the QTI and considers the possible arrhythmogenic potential of the short QTI.

journal_name

Cardiology

journal_title

Cardiology

authors

Gussak I,Brugada P,Brugada J,Wright RS,Kopecky SL,Chaitman BR,Bjerregaard P

doi

10.1159/000047299

subject

Has Abstract

pub_date

2000-01-01 00:00:00

pages

99-102

issue

2

eissn

0008-6312

issn

1421-9751

pii

47299

journal_volume

94

pub_type

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