Abstract:
:Characteristic biliary tree abnormalities in metachromatic leukodystrophy (MLD) include gallbladder polyposis and haemobilia. We report two brothers with MLD, who presented with uncommon biliary complications. One presented with gastric outlet obstruction secondary to gallbladder enlargement, which was treated by percutaneous aspiration. He later developed gallbladder carcinoma with liver metastases. His brother demonstrated US findings consistent with gallstones.
journal_name
Pediatr Radioljournal_title
Pediatric radiologyauthors
Simanovsky N,Ackerman Z,Kiderman A,Fields Sdoi
10.1007/s002470050446subject
Has Abstractpub_date
1998-09-01 00:00:00pages
706-8issue
9eissn
0301-0449issn
1432-1998journal_volume
28pub_type
杂志文章abstract::Ultrasound (US) has been proposed as an alternative first-line imaging modality to diagnose community-acquired pneumonia in children. Lung US has the potential benefits over chest radiography of being radiation free, subject to fewer regulatory requirements, relatively lower cost and with immediate bedside availabilit...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-017-3910-1
更新日期:2017-10-01 00:00:00
abstract::We report a case of a child with D-transposition of the great arteries treated with prostaglandin E1 (PGE1) who subsequently developed extensive brown fat necrosis. To the best of our knowledge, no previous association among congenital heart disease, PGE1, and brown fat necrosis has been reported. ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s002470050536
更新日期:1999-01-01 00:00:00
abstract::A case of vein of Galen aneurysm, studied with a fast gradient refocusing pulse MRI sequence, is presented. Fast MRI sequences allowed the acquisition of additional hemodynamic information that was not available with either routine MRI or angiography. ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02013833
更新日期:1993-01-01 00:00:00
abstract::The detailed radiographic features of triploidy, a fatal congenital disorder with 69 chromosomes, have not previously been reported. Radiographs of ten liveborn infants with chromosomally confirmed triploidy showed six findings highly suggestive of this diagnosis: harlequin orbits, small anterior fontanelle, gracile r...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02386842
更新日期:1989-01-01 00:00:00
abstract:BACKGROUND:Sclerotic bone lesions are often seen on chest CT in adults with tuberous sclerosis complex. OBJECTIVE:To characterize bone lesions at abdominal MRI in children with tuberous sclerosis complex. MATERIALS AND METHODS:This retrospective review included 70 children with tuberous sclerosis complex who had unde...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-016-3549-3
更新日期:2016-05-01 00:00:00
abstract::Occasionally, heterotopic splenic tissue can occur in the renal fossa secondary to splenosis following splenic trauma or splenectomy. Rarely, it can represent a developmental anomaly secondary to fusion of splenic and renal tissues. Splenorenal fusion can present as a renal mass, mimicking primary or secondary renal n...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-009-1201-1
更新日期:2009-07-01 00:00:00
abstract:BACKGROUND:A pull-back tube esophagogram (PBTE) is widely accepted in the literature as the radiological investigation of choice for the diagnosis of tracheoesophageal fistula without esophageal atresia. However, PBTE is rarely performed in our institution, as we have been successful in confirming the presence of such ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-006-0269-0
更新日期:2006-11-01 00:00:00
abstract::Hepatocyte-specific contrast media are gadolinium chelates that are taken up by hepatocytes and partially cleared via the biliary tree. The absence of lesional uptake of the contrast media in the hepatobiliary phase is a marker of either the absence of hepatocytes or of poorly functioning, neoplastic hepatocytes. Upta...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-018-4108-x
更新日期:2018-08-01 00:00:00
abstract::Magnetic resonance enterography (MRE) now plays a central role in diagnosing pediatric inflammatory bowel disease (IBD), and its role in other intestinal pathologies such as scleroderma is gradually expanding. MRE helps distinguish between Crohn disease and ulcerative colitis, defining extent and severity. Standard MR...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-016-3596-9
更新日期:2016-05-01 00:00:00
abstract:BACKGROUND:Image-guided percutaneous core needle biopsy (PCNB) of soft-tissue lesions is a minimally invasive technique that can provide a definitive diagnosis for treatment. Anatomical and age considerations in children require judicious use of safe percutaneous biopsy techniques. There are, however, limited data on t...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-015-3364-2
更新日期:2015-09-01 00:00:00
abstract::The clinical and radiological findings in fused labia are described. Some of the patients were asymptomatic. The others were referred because of a suspicion of urinary infection. Micturating cystourethrography showed collection of contrast material above the labia and marked reflux into the vagina in all patients exam...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF00975335
更新日期:1978-04-10 00:00:00
abstract::An otherwise healthy 11-month-old boy presented with bilateral abdominal masses. Imaging findings, differential diagnosis, histological findings, and pertinent discussion are presented. ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s002470050197
更新日期:1997-07-01 00:00:00
abstract::The authors review their experience with transrectal drainage of pelvic abscesses in seven children and adolescents (6-16 years old). Initial access was guided by transrectal ultrasound with an endovaginal transducer followed by fluoroscopy for placement of self-retaining catheters (8.5-10 F) using the Seldinger techn...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF03178041
更新日期:1996-12-01 00:00:00
abstract::A newborn suffered immediate neonatal respiratory distress because of an obstructive, soft-tissue nasal mass. Clinical examination revealed a cleft palate with a protruding polypoid mass. CT and MRI showed a heterogeneous nasopharyngeal mass and associated intracranial abnormalities - duplication of the hypophysis and...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s002470050354
更新日期:1998-05-01 00:00:00
abstract::Pseudoaneurysms (PAn) are uncommon in adults and even less common in children. They are most often encountered after iatrogenic arterial injury. Presentation may be substantially delayed after the iatrogenic event, and diagnosis can be difficult, especially when the PAn occurs in an unexpected location. Treatment of P...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-004-1320-7
更新日期:2005-04-01 00:00:00
abstract::The purpose of this report is to describe imaging findings in activated protein C resistance, a hereditary cause of recurrent thrombosis. The case described was unusual in that a neonate was affected, whereas the vast majority of cases occur in adulthood. This entity is important to diagnose because of the recurrent n...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s002470050424
更新日期:1998-08-01 00:00:00
abstract::Pediatric radiologists in 40 children's hospitals in North America were interviewed to determine their choice of contrast media in the diagnosis and treatment of intussusception. The respondents indicated that barium was utilized in the vast majority of instances. Almost all indicated that they would proceed with bari...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02467295
更新日期:1989-01-01 00:00:00
abstract:BACKGROUND:Anteriorly displaced anus is an anomaly that is debated with regard to its nomenclature, diagnosis and management. OBJECTIVE:To describe MRI anatomy of the anal canal in children with anteriorly displaced anus and its impact on the process of defecation. MATERIALS AND METHODS:We prospectively examined ten ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-014-2897-0
更新日期:2014-07-01 00:00:00
abstract::A marked thoracic deformity associated with intrathoracic tracheal narrowing was seen in a 17-year-old with achondroplasia and dyspnea. The role of chest deformity and its evaluation by CT and MRI in achondroplastic patients with respiratory symptoms are considered. ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02012508
更新日期:1992-01-01 00:00:00
abstract::Paternal uniparental disomy for chromosome 14 (patUPD14) is a rare condition, this being the eighth report. A male infant, born prematurely, was noted to have extremely lax skin and bilateral inguinal hernias. Skin biopsy confirmed the clinical diagnosis of congenital cutis laxa, but this did not explain the limb abno...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-003-0931-8
更新日期:2003-07-01 00:00:00
abstract::In this report, the clinical and unusual sonographic manifestations of a perforated appendiceal abscess is described. ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02467309
更新日期:1989-01-01 00:00:00
abstract::Castleman's disease is a benign lymphoproliferative disorder characterised by enlarged hyperplastic lymph nodes. It is rare in children and usually presents as localised disease. Subpectoral involvement has not been previously described in multicentric Castleman's disease in children. We present the CT, US and Doppler...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-003-0947-0
更新日期:2003-08-01 00:00:00
abstract:BACKGROUND:Subglottic haemangioma causes progressive and life-threatening stridor, typically manifesting at age 2-3 months. Standard diagnosis is by laryngoscopy. Larynx sonography is rarely used but allows assessment of the presence and extension of a mass that impinges on the subglottic airway. The additional use of ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-011-2213-1
更新日期:2011-11-01 00:00:00
abstract:BACKGROUND:Magnetic resonance imaging (MRI) usage has anecdotally increased due to the principles of ALARA and the desire to Image Gently. Aside from a single abstract in the emergency medicine literature, pediatric emergency department MRI usage has not been described. OBJECIVE:Our objective was to determine whether ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-016-3764-y
更新日期:2017-03-01 00:00:00
abstract::This retrospective study documents the incidence and distribution of fractures in 117 children with end-stage liver disease who underwent orthotopic liver transplantation (OLT) over a 6-year period (1987-1993). Both the pre- and post-OLT phases were included. Nineteen children (16.2 %) sustained a total of 69 fracture...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:
更新日期:1995-11-01 00:00:00
abstract::A rare, elusive, mobile, pedunculated nasopharyngeal tumor in a neonate is described. The child was only intermittently symptomatic and the diagnosis was not made until 1 month of age. ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02389013
更新日期:1988-01-01 00:00:00
abstract::The neonate in this report had severe encephalotrigeminal angiomatosis with intracranial calcification, cranial hemiatrophy, microcephaly and generalised severe cerebral atrophy. Such findings are not common in the newborn with this syndrome. ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF00973676
更新日期:1979-02-26 00:00:00
abstract:BACKGROUND:Balloon dilatation of the oesophagus in children has been performed predominantly for treating strictures, which are the result of primary repair of oesophageal atresia, interposition surgery or restrictive Nissen's fundoplication. Reports of the use of this technique for alternative causes of stricture are ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-003-1011-9
更新日期:2003-10-01 00:00:00
abstract::Antenatal detection of mesoblastic nephroma by US is possible. Reviewing the literature, we found 19 previously reported cases, only 1 of which underwent prenatal MRI. We present a further case diagnosed by US and confirmed with MRI. The imaging findings and differential diagnoses are discussed. Early and correct dete...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s002470050033
更新日期:2000-03-01 00:00:00
abstract:BACKGROUND:Size-specific dose estimate is gaining increased acceptance as the preferred index of CT dose in children. However it was developed based on non-clinical data. OBJECTIVE:To compare the accuracy of size-specific dose estimate (SSDE) based on geometric and body weight measures in pediatric chest and abdomen C...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-016-3604-0
更新日期:2016-08-01 00:00:00