Unusual gallbladder findings in two brothers with metachromatic leukodystrophy.

Abstract:

:Characteristic biliary tree abnormalities in metachromatic leukodystrophy (MLD) include gallbladder polyposis and haemobilia. We report two brothers with MLD, who presented with uncommon biliary complications. One presented with gastric outlet obstruction secondary to gallbladder enlargement, which was treated by percutaneous aspiration. He later developed gallbladder carcinoma with liver metastases. His brother demonstrated US findings consistent with gallstones.

journal_name

Pediatr Radiol

journal_title

Pediatric radiology

authors

Simanovsky N,Ackerman Z,Kiderman A,Fields S

doi

10.1007/s002470050446

subject

Has Abstract

pub_date

1998-09-01 00:00:00

pages

706-8

issue

9

eissn

0301-0449

issn

1432-1998

journal_volume

28

pub_type

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