Abstract：
:Peroneal muscular atrophy (Charcot-Marie-Tooth-disease) is a hereditary disease of the peripheral motor and sensory neurons. In most patients the distal extremities are affected but involvement of the cranial nerves has also been described. We describe a 58 year old patient suffering from this disease accompanied by bilateral hearing loss. Audiometric examinations over a period of 10 years showed no progression and indicate a neural hearing loss. This was finally verified by auditory potentials (EAEP); J V and J III were prolonged, indicating a neural origin of hearing loss. Thus the lesion must be localised to the cranial nerves or brainstem and represent a symptom of the peroneal muscular atrophy.
journal_name
HNOjournal_title
HNOauthors
Laubert Asubject
Has Abstractpub_date
1986-10-01 00:00:00pages
434-7issue
10eissn
0017-6192issn
1433-0458journal_volume
34pub_type
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