Abstract:
:A malignant tumor of striated muscle origin, rhabdomyosarcoma (RMS) is a childhood tumor that has benefited from nearly 30 years of multimodality therapy, culminating in a >70% overall 5-year survival. Prognosis for RMS is dependent on primary tumor site, age, completeness of resection, presence and number of metastatic sites, histology, and biology of the tumor cells. Multimodality treatment is based on risk stratification according to pre-treatment stage, postoperative group, histology, and site. Unique to RMS is the concept of postoperative clinical grouping that assesses the completeness of disease resection and takes into account lymph node evaluation at both the regional and metastatic basins. At all sites, if complete operative resection of disease is accomplished, including microscopic disease, survival is improved. Therefore, the surgeon plays a vital role in determining risk stratification for treatment, local control of the primary tumor and overall outcome for the patient with RMS.
journal_name
Semin Pediatr Surgjournal_title
Seminars in pediatric surgeryauthors
Dasgupta R,Fuchs J,Rodeberg Ddoi
10.1053/j.sempedsurg.2016.09.011subject
Has Abstractpub_date
2016-10-01 00:00:00pages
276-283issue
5eissn
1055-8586issn
1532-9453pii
S1055-8586(16)30049-Xjournal_volume
25pub_type
杂志文章,评审abstract::During the past 10 years, the minimally invasive technique has become the standard approach for many thoracic, abdominal, and pelvic procedures in adults and children. We now know there are well-defined benefits to this approach. However, when it was introduced, the laparoscopic technique was quickly adopted without a...
journal_title:Seminars in pediatric surgery
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journal_title:Seminars in pediatric surgery
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journal_title:Seminars in pediatric surgery
pub_type: 杂志文章,评审
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journal_title:Seminars in pediatric surgery
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journal_title:Seminars in pediatric surgery
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journal_title:Seminars in pediatric surgery
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journal_title:Seminars in pediatric surgery
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journal_title:Seminars in pediatric surgery
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journal_title:Seminars in pediatric surgery
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journal_title:Seminars in pediatric surgery
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journal_title:Seminars in pediatric surgery
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journal_title:Seminars in pediatric surgery
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journal_title:Seminars in pediatric surgery
pub_type: 杂志文章,评审
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journal_title:Seminars in pediatric surgery
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journal_title:Seminars in pediatric surgery
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journal_title:Seminars in pediatric surgery
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journal_title:Seminars in pediatric surgery
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journal_title:Seminars in pediatric surgery
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journal_title:Seminars in pediatric surgery
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