Abstract：
:A 10-year old, mentally and physically normally developed girl complained of back pain following an accident. Radiological findings revealed an inhomogeneous, coarse osteosclerosis along the endplates and posterior parts of the ovoid shaped vertebral bodies, in the proximal and distal femora-, proximal humeri and tibia epiphyses, and along the lateral aspects of the femoral necks. The pelvis presented a mottled appearance of the trabecular pattern at the symphysis pubis and the lateral parts of ischii and sclerosis in the acetabular region. The only laboratory abnormality was a high serum parathormone level. The family history revealed an autosomal dominant inheritance. The name proposed by Maroteaux for this skeletal disorder is osteomesopycnosis, as the lesions were localized to the spine, pelvis and sometimes proximal femur. The skull, ribs, long bones, hands and feet were not involved in the reported 12 cases. Radiographs of this patient showed in addition changes in the hand. This disease must be distinguished from atypical axial osteomalacia.
journal_name
Pediatr Radioljournal_title
Pediatric radiologyauthors
Schmidt H,Mannkopf H,Ullrich K,von Lengerke HJdoi
10.1007/BF02387669subject
Has Abstractpub_date
1989-01-01 00:00:00pages
489-92issue
6-7eissn
0301-0449issn
1432-1998journal_volume
19pub_type
杂志文章abstract：:Rapidly involuting congenital hemangioma (RICH) is a recently recognized entity in which the vascular tumor is fully developed at birth and undergoes rapid involution. Angiographic findings in two infants with congenital hemangioma are reported and compared with a more common postnatal infantile hemangioma and a conge...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-002-0726-3
更新日期：2003-01-01 00:00:00
abstract：BACKGROUND:Accurate diagnosis of hepatic vein (HV) stenosis by real-time and color Doppler US (CD-US) after segmental liver transplantation in children can decrease morbidity because it allows unnecessary biopsy, obstruction or thrombosis and loss of the graft to be avoided. OBJECTIVE:To evaluate CD-US parameters to p...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-007-0731-7
更新日期：2008-04-01 00:00:00
abstract：BACKGROUND:Pediatric optic pathway gliomas are typically indolent but have a variable clinical course. Treatment is dictated by symptoms and changes on contrast-enhanced MRI examinations. Gadolinium retention in children has motivated parsimonious use of gadolinium-based contrast agents. OBJECTIVES:To determine survei...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-018-4154-4
更新日期：2018-09-01 00:00:00
abstract：:An unusual case is presented of a vascular ring due to a right arch with mirror-image branching and a left ligamentum arteriosum from the descending aorta to the left pulmonary artery. There have been only four previous reports of this rare arch anomaly. In addition, the patient had no underlying congenital heart lesi...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/BF02019065
更新日期：1995-01-01 00:00:00
abstract：:Ultrasound is a remarkably powerful and versatile modality for pediatric imaging, without requiring exposure to radiation or sedatives. By providing information on blood flow, Doppler sonography can reveal details about normal physiology and disease processes not discernable from gray-scale anatomic images alone. Howe...
journal_title：Pediatric radiology
pub_type： 杂志文章,评审
doi：10.1007/s00247-004-1228-2
更新日期：2004-10-01 00:00:00
abstract：:Vasoactive intestinal polypeptide (VIP) secreting neural crest tumours are an uncommon but important treatable cause of intractable childhood diarrhoea. The radiological appearances of two cases are presented with a review of radiological findings in childhood VIP secreting neural crest tumours. Twenty eight cases of ...
journal_title：Pediatric radiology
pub_type： 杂志文章,评审
doi：10.1007/BF02011377
更新日期：1990-01-01 00:00:00
abstract：:Isolated, well-differentiated ectopic cerebellar tissue is extremely rare, with only eight cases in the literature. We describe a unique case of histopathologically proven ectopic cerebellar tissue presenting as a discrete extra-axial mass in the posterior cranial fossa. We describe the clinical, CT and MRI findings, ...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-012-2411-5
更新日期：2012-11-01 00:00:00
abstract：:A case of pyelocalyceal diverticula in a patient with the Beckwith-Wiedemann syndrome is presented. The abnormalities were first identified on screening ultrasound and confirmed at excretory urography. The diverticula in this syndrome are likely secondary to hereditary embryopathy of the kidneys. ...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/BF02386605
更新日期：1987-01-01 00:00:00
abstract：:The logistic approach in diagnosis of focal nodular hyperplasia (FNH) of the liver is discussed, based on the experience with three children. In only one child could the diagnosis be made without angiography. In that child the combination of hypervascularity on the radionuclide angiogram and uptake of the radiocolloid...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/BF02390106
更新日期：1983-01-01 00:00:00
abstract：:Pseudotumoral cystitis is an unusual lesion and since it may be confused with rhabdomyosarcoma, knowledge of its existence is important. We report eight cases. ...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：
更新日期：1993-01-01 00:00:00
abstract：:The article "Inter- and intra-observer reliability of contrast-enhanced magnetic resonance imaging parameters in children with suspected juvenile idiopathic arthritis of the hip". ...
journal_title：Pediatric radiology
pub_type： 杂志文章,已发布勘误
doi：10.1007/s00247-018-4285-7
更新日期：2018-12-01 00:00:00
abstract：:In order to evaluate the role of gadolinium-DOTA enhanced MRI in the management of painful osseous crises in children with sickle cell anemia (SCA), nine children with SCA underwent MRI, bone scans and ultrasonographic studies during 11 osseous crises. Imaging findings were compared with the final diagnosis: three acu...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/BF02020160
更新日期：1994-01-01 00:00:00
abstract：:Neuroblastomas are the most common extracranial solid malignancy in children. In contrast, salivary gland tumors are uncommon in children, accounting for only 1% of all pediatric neoplasms. Parotid metastases are rare; only two cases of parotid metastases from neuroblastomas have been reported with an emphasis on the ...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-010-1750-3
更新日期：2010-12-01 00:00:00
abstract：:Intrathecal baclofen has long been known to be an efficacious treatment of spasticity in children with cerebral palsy. Test bolus administration is often necessary to ensure patients will benefit from this treatment. The introduction of a intrathecal catheter for test bolus administration can prove challenging in a su...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-017-3816-y
更新日期：2017-05-01 00:00:00
abstract：:We report an extremely unusual case of a 4-month-old boy who presented with a sudoriferous gland cyst of the orbit. Congenital sudoriferous cyst is extremely rare in both the adult and pediatric populations. The CT and MRI findings are presented and the pertinent literature reviewed. ...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-005-1523-6
更新日期：2005-11-01 00:00:00
abstract：:Purpose. To determine whether gadolinium-enhanced MR imaging can detect early reversible ischemia of the capital femoral epiphysis and physis induced by hip hyperabduction in piglets. Materials and methods. Thirteen 1- to 3-week-old piglets were placed in maximal abduction of both hips and studied with dynamic gadolin...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/BF02011824
更新日期：1995-01-01 00:00:00
abstract：:Radiologically visible calcification in the wall of a uriniferous perirenal pseudocyst is rare. This unusual finding was seen in a newborn infant who was found to have a left flank mass on the first day of life. When perirenal pseudocysts occur in infants, they are usually caused by congenital obstructive lesions of t...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/BF00973970
更新日期：1980-01-01 00:00:00
abstract：:Narrow duplicated internal auditory canal (IAC) is a rare malformation of the temporal bone that is associated with ipsilateral congenital sensorineural hearing loss. This may be an isolated finding or a part of a syndrome. Radiological examination should demonstrate aplasia or hypoplasia of the neural components of t...
journal_title：Pediatric radiology
pub_type： 杂志文章,评审
doi：10.1007/s00247-005-1547-y
更新日期：2005-12-01 00:00:00
abstract：:Sickle cell disease is a major cause of pediatric stroke. Understanding the disease that affects the brain as infarctions, both clinically apparent and silent, requires an understanding of how the blood vessels are affected, the way in which both the brain and the blood vessels are imaged by MRI and MRA and the mechan...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-005-1420-z
更新日期：2005-03-01 00:00:00
abstract：:As the need for accurate diagnostic imaging often continues throughout a cancer survivor's life, imaging methods with the least toxicity must be used so as to provide needed information without contributing to long-term sequelae that might compound toxicities inherent with the primary disease and its treatment. In thi...
journal_title：Pediatric radiology
pub_type： 杂志文章,评审
doi：10.1007/s00247-011-2108-1
更新日期：2011-09-01 00:00:00
abstract：:Gonadal dysgenesis and coarctation of the aorta were found in four patients to be associated with premature sternal fusion but possible etiologic relationship to shield chest deformity in suggested. ...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/BF02386775
更新日期：1985-01-01 00:00:00
abstract：:Cancer predisposition syndromes increase the incidence of tumors during childhood and are associated with significant morbidity and mortality. Imaging is paramount for ensuring early detection of neoplasms, impacting therapeutic interventions and potentially improving outcome. While conventional imaging techniques inv...
journal_title：Pediatric radiology
pub_type： 杂志文章,评审
doi：10.1007/s00247-019-04431-3
更新日期：2019-10-01 00:00:00
abstract：:Two patients with different patterns of soft tissue and bone involvement demonstrate the variability of extracutaneous manifestations of juvenile xanthogranuloma, a non-X histiocytosis, better known to dermatologists than to radiologists. ...
journal_title：Pediatric radiology
pub_type： 杂志文章,评审
doi：10.1007/BF02016261
更新日期：1992-01-01 00:00:00
abstract：:We present a case of blow-out fracture of the superomedial orbital wall in a 6-year-old boy. The initial plain radiograph showed an intact orbital margin and opacification of the ethmoid sinus. A fine-cut CT scan of the facial bones revealed a complex fracture of the medial orbital wall extending into the orbital roof...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-009-1280-z
更新日期：2009-08-01 00:00:00
abstract：:Certain misleading appearances are peculiar to pediatric uroradiology. The most frequently encountered pitfalls are related to the bladder, to vesicoureteral reflux, and to the duplicated collecting system. The bi-chambered nature of the child's bladder, and the rapid settling of contrast material to the most dependen...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/BF01644339
更新日期：1980-09-01 00:00:00
abstract：:We describe the technique of partial liquid ventilation and outline its indications. We present our imaging experience with this infrequently used therapy using a wide variety of radiographs from neonatal and adult patients. The radiographic appearance of white lungs, due to the perfluorocarbons used in partial liquid...
journal_title：Pediatric radiology
pub_type： 杂志文章,评审
doi：10.1007/s00247-005-1548-x
更新日期：2005-11-01 00:00:00
abstract：:Imaging studies for sinusitis add little to the clinical management of the pediatric patient in most instances. The findings shown by paranasal sinus imaging are nonspecific and need to be correlated with clinical findings. Coronal CT is recommended for complications or for recurrent or persistent sinus disease. ...
journal_title：Pediatric radiology
pub_type： 杂志文章,评审
doi：10.1007/s002470050251
更新日期：1997-11-01 00:00:00
abstract：:Airway compression is a common problem in children with certain forms of congenital heart disease. Although various surgical approaches are available to overcome this form of airway obstruction, internal stenting is necessary in a minority of patients. It can be difficult to assess the success of stenting at the time ...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-006-0174-6
更新日期：2006-08-01 00:00:00
abstract：:We used the fast field-echo technique of magnetic resonance (MR) imaging with an intravenous bolus injection of paramagnetic contrast agent to evaluate glomerular function. The time-dependent curves of changes in signal intensity observed in the renal cortex and renal medulla brought about by the paramagnetic contrast...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/BF01395707
更新日期：1996-01-01 00:00:00
abstract：:The incidental detection of small lung nodules in children is a vexing consequence of an increased reliance on CT. We present an algorithm for the management of lung nodules detected on CT in children, based on the presence or absence of symptoms, the presence or absence of elements in the clinical history that might ...
journal_title：Pediatric radiology
pub_type： 杂志文章,评审
doi：10.1007/s00247-014-3269-5
更新日期：2015-04-01 00:00:00
