Persistent Truncus Arteriosus With Intact Ventricular Septum: Clinical, Hemodynamic and Short-term Surgical Outcome.

Abstract:

INTRODUCTION:Truncus arteriosus with intact ventricular septum is a rare and unique variant of persistent truncus arteriosus (PTA) which usually presents with central cyanosis and congestive heart failure in neonate and early infancy. Associated cardiac and non-cardiac anomalies may affect morbidity and mortality of these patients. CASE PRESENTATION:We describe clinical presentation, echocardiography and angiographic features of a 7-month old boy with PTA and intact ventricular septum who underwent surgical repair of the anomaly at our institution. Operative findings, surgical procedure and short-term outcome are reported. CONCLUSIONS:While our patient had systemic pulmonary arterial pressure at the time of complete surgical repair, it was improved after surgery.

journal_name

Iran J Pediatr

authors

Ajami G,Amirghofran AA,Amoozgar H,Borzouee M

doi

10.5812/ijp.2081

subject

Has Abstract

pub_date

2015-10-01 00:00:00

pages

e2081

issue

5

eissn

2008-2142

issn

2008-2150

journal_volume

25

pub_type

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