CVID enteropathy- a rare cause of chronic diarrhea in a child.

Abstract:

:Common variable immunodeficiency (CVID) is a rare primary immunodeficiency disease characterized by hypogammaglobulinemia and recurrent bacterial infections especially in respiratory and gastrointestinal systems. The authors present here a case of CVID with uncommon gastrointestinal manifestation in the form of CVID enteropathy. Based upon the clinical presentation and histopatholic findings the patient was diagnosed as CVID enteropathy and treated with intravenous antibiotics and 3-4 wkly intravenous immunoglobulin infusion and he had responded poorly to gastrointestinal symptoms but the frequency of respiratory and skin infection reduced. CVID has heterogenous gastrointestinal manifestations; among them the CVID enteropathy is an uncommon presentation which responds poorly to the mainstay therapy of intravenous immunoglobulin infusion and represents a diagnostic as well as therapeutic challenge for treating physician.

journal_name

Indian J Pediatr

authors

Patel J,Kumar A,Agasti A,Choksey A,Phadke A,Sawant P

doi

10.1007/s12098-011-0635-2

subject

Has Abstract

pub_date

2012-10-01 00:00:00

pages

1374-6

issue

10

eissn

0019-5456

issn

0973-7693

journal_volume

79

pub_type

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