Abstract:
:A study of prevalence and aetiology was performed on 63 children and 127 adults in Denmark with congenital deafblindness. Using a Scandinavian definition of deafblindness, the prevalence of congenital deafblindness was found to be 1:29 000. Thirty-five different aetiological causes of deafblindness were found. Causes of congenital deafblindness were different among adults compared to causes among children. Rubella syndrome (28%, n = 36) and Down syndrome (8%. n = 10) were the largest groups among people above 18 years of age. Among children CHARGE syndrome (16%, n = 13) was the largest group. Ethnicity was also evaluated. Among children 72% were Danish, but among the adults 98% were Danish. Implications of difference in aetiology and ethnicity are discussed in relation to the Scandinavian traditions of clinical practice and identification of congenital deafblindness.
journal_name
Int J Audioljournal_title
International journal of audiologyauthors
Dammeyer Jdoi
10.3109/14992020903311388subject
Has Abstractpub_date
2010-02-01 00:00:00pages
76-82issue
2eissn
1499-2027issn
1708-8186journal_volume
49pub_type
杂志文章abstract:OBJECTIVE:To investigate total leisure noise exposure among adolescents and to assess its association with hearing. DESIGN:Based on self-reported time spent on 19 leisure activities and associated mean sound pressure levels reported in the literature, total leisure noise exposure was evaluated and compared to noise at...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992027.2015.1030510
更新日期:2015-01-01 00:00:00
abstract::In a laboratory study, we found that normal-hearing and hearing-impaired listeners preferred less than normal overall calculated loudness (according to a loudness model of Moore & Glasberg, 1997). The current study verified those results using a research hearing aid. Fifteen hearing-impaired and eight normal-hearing p...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992020500190177
更新日期:2006-01-01 00:00:00
abstract:OBJECTIVE:Recent studies have shown that the frequency-following response (FFR) to voice pitch can be a useful method to evaluate the signal-processing mechanisms and neural plasticity in the human brainstem. The purpose of this study was to examine the quantitative properties of the FFR trends with an exponential curv...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992027.2011.582164
更新日期:2011-09-01 00:00:00
abstract::Children with listening difficulties, but normal audiometry, may be diagnosed with APD. The diagnosis is typically based on poor performance on tests of perception of both non-speech and speech stimuli. However, non-speech test results correlate only weakly with evaluations of speech-in-noise processing, cognitive ski...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992027.2012.723143
更新日期:2013-01-01 00:00:00
abstract::The real-ear insertion response (REIR) of a hearing aid is estimated as the difference between the aided response and the unaided response in the ear canal. Changes in the position of the loudspeaker relative to the head, between the two measurements, may reduce the accuracy of the estimate. The spatial variability of...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992020400050036
更新日期:2004-05-01 00:00:00
abstract:OBJECTIVE:To examine the effectiveness of targeted surveillance for the identification of moderate-profound PCHI in babies who pass the newborn hearing screen in England and have risk factors. DESIGN:Retrospective analysis. STUDY SAMPLE:2,307,880 children born 01/04/06-30/09/09 in England. RESULTS:Overall the preval...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992027.2013.769067
更新日期:2013-06-01 00:00:00
abstract::This study aimed to determine if adolescents/young adults gained additional perceptual benefit from sequential bilateral cochlear implants within 12 months, and to document adaptation to the second implant. Assessments comprised a pediatric version of The Speech, Spatial and Qualities of Hearing Scale (SSQ), anecdotal...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992020903470767
更新日期:2010-05-01 00:00:00
abstract::The purpose of this study was to understand the parental perspective on paediatric cochlear implantation over time. Face-to-face semi-structured interviews were conducted with 216 families of children who were implanted at the Nottingham Paediatric Cochlear Implant Programme between 1989 and 2002, and who were attendi...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992020500146500
更新日期:2005-07-01 00:00:00
abstract::The aim of the present study was to investigate the consequences of chronic otitis media on inner ear function. Retrospective analysis of conventional pure-tone audiometry tests was carried out on 344 patients who were scheduled for surgical treatment of unilateral chronic otitis media without other risk factors for s...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992020500243737
更新日期:2005-10-01 00:00:00
abstract:OBJECTIVE:The study aims to compare the performance of hearing aids fitted according to the NAL-NL1 and DSL v5 prescriptive procedure for children. DESIGN:This is a crossover four period trial. STUDY SAMPLE:Sixteen school-aged children with moderately severe to profound hearing losses participated in the study. The c...
journal_title:International journal of audiology
pub_type: 杂志文章,随机对照试验
doi:10.3109/14992027.2012.755740
更新日期:2013-05-01 00:00:00
abstract::Objective: To clarify the distinction between Auditory Processing Disorder (APD) and Attention Deficit Disorder (ADD) using the CHC Model.Design: A cross-sectional study compared responses of caregivers about their children's behaviour to identify characteristics of APD (CHC Model) and ADD (DSM-5).Study Sample: Caregi...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992027.2019.1682199
更新日期:2020-03-01 00:00:00
abstract::The objective of this study was to explore cochlear implant users' speech perception performance in quiet and in noise for low to moderate stimulation rates. Eight postlingually deaf adult users of the Nucleus CI24 cochlear implant (contour electrode array) using the ESPrit 3G speech processor participated in this stu...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992020902858967
更新日期:2009-08-01 00:00:00
abstract:OBJECTIVE:The primary purpose of the study was to compare intervention approaches for children with auditory processing disorder (APD): bottom-up training including activities focused on auditory perception, discrimination, and phonological awareness, and top-down training including a range of language activities. Anot...
journal_title:International journal of audiology
pub_type: 杂志文章,随机对照试验
doi:10.3109/14992027.2012.670272
更新日期:2012-07-01 00:00:00
abstract:OBJECTIVE:Using a dual task paradigm, two experiments were conducted to: (1) quantify the listening effort that young and older adults expend to recognize speech in noise when presented under audio-only (Experiment 1) and audiovisual conditions (Experiment 2) and, (2) determine the influence visual cues have on listeni...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992027.2011.599870
更新日期:2011-11-01 00:00:00
abstract::The purpose of this study was to evaluate cisplatin-induced ototoxicity and the protective effects of tiopronin. Twenty-four adult Wistar rats served as subjects and were divided into three groups. Eight rats receiving only saline (group A) were used as controls. Eight rats received cisplatin (2 mg/kg) injections (gro...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992020400050059
更新日期:2004-09-01 00:00:00
abstract:OBJECTIVE:We report a case study on possible alterations in resting-state functional connectivity between the auditory network and non-auditory brain regions in tinnitus patients. DESIGN:Independent component analyses were performed to evaluate coherent spontaneous activity in distributed brain networks. The resting-s...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992027.2011.652677
更新日期:2012-05-01 00:00:00
abstract::In 1997, Don and his co-workers described a new method for evaluating the auditory brainstem response (ABR)--yielding the stacked-wave-V ABR--which may permit the reliable detection of even small vestibular schwannomas (VSs). However, this method requires a masking technique that may not be readily available to the cl...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992020309078338
更新日期:2003-03-01 00:00:00
abstract:OBJECTIVE:The current study investigates the extent to which the linguistic complexity of three commonly employed speech recognition tests and second language proficiency influence speech recognition thresholds (SRTs) in noise in non-native listeners. DESIGN:SRTs were measured for non-natives and natives using three G...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992027.2015.1063715
更新日期:2015-01-01 00:00:00
abstract:OBJECTIVE:To assess the American Medical Association (AMA) guide to the evaluation of binaural hearing impairment (BHI) as a procedure for estimating severity of hearing loss from audiograms. DESIGN:The BHIs of Australian war veterans were calculated from their hearing threshold levels (HTLs) and compared with their s...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992027.2013.821208
更新日期:2013-11-01 00:00:00
abstract:OBJECTIVES:To introduce the Italian adaptation of the STARR test based on a roving-level adaptive method to mimic challenging real-life listening conditions for use in people with auditory prostheses. DESIGN:Normative data were collected and interlist-variability, as well as learning effects, were investigated using a...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992027.2015.1124296
更新日期:2016-01-01 00:00:00
abstract:OBJECTIVE:The SCAN-A ( Keith, 1994 ) is a test for auditory processing disorders in adolescents aged 11+ and adults developed in the USA. It was previously found that the children's version (the SCAN-C) over diagnoses auditory processing disorder in UK children. This study was conducted to assess the use of the SCAN-A ...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992027.2010.527861
更新日期:2011-02-01 00:00:00
abstract::Objective: This clinical note describes the Individualised - Active Communication Education (I-ACE) programme designed to improve problem solving and self-management in adults with hearing impairment. Design: The I-ACE was offered to adult clients seeking help for the first time and effects were measured for participa...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992027.2019.1587180
更新日期:2019-08-01 00:00:00
abstract:OBJECTIVE:To validate the hyperacusis questionnaire (HQ) in different strata of emotional exhaustion (EE). DESIGN:HQ-scores and uncomfortable loudness levels (ULLs) were assessed in 348 individuals (140 men and 208 women) with low, intermediate, and high EE-levels. RESULTS:Four individuals (1.1%) met the critical val...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992027.2012.695874
更新日期:2012-10-01 00:00:00
abstract:OBJECTIVE:To consider the evolving concept of auditory processing disorder (APD). DESIGN:Narrative review and opinion piece. STUDY SAMPLE:Eight approaches to APD described in the literature and its definitions by ten societies or groups from around the world. RESULTS:The dominant conceptualisation of APD remains one...
journal_title:International journal of audiology
pub_type: 杂志文章,评审
doi:10.1080/14992027.2017.1409438
更新日期:2018-04-01 00:00:00
abstract::This paper presents normative data of hearing threshold levels of a population screened with various criteria, as compared to unscreened population data. Computer-controlled pure-tone audiometry was administered to the adult population in Nord-Trøndelag County, Norway, during 1995-1997. The 51975 participants also pro...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992020500057731
更新日期:2005-04-01 00:00:00
abstract:OBJECTIVE:Working memory refers to a cognitive system that manages information processing and temporary storage. Recent work has demonstrated that individual differences in working memory capacity measured using a reading span task are related to ability to recognize speech in noise. In this project, we investigated wh...
journal_title:International journal of audiology
pub_type: 杂志文章,多中心研究
doi:10.3109/14992027.2015.1043062
更新日期:2015-01-01 00:00:00
abstract::We compared two adaptive procedures for fitting a multi-channel compression hearing aid. "Camadapt" uses judgements of the loudness of speech stimuli and the tonal quality of music stimuli. "Eartuner" uses judgements of the loudness and clarity of speech stimuli with differing spectral characteristics. Sixteen new use...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992020500060198
更新日期:2005-06-01 00:00:00
abstract::We evaluated the benefits of fast-acting WDRC, slow-acting AVC, and linear reference fittings for speech intelligibility and reported disability, in a within-subject within-device masked crossover design on 50 listeners with SNHL. Five hearing aid fittings were implemented having two compression channels and seven fre...
journal_title:International journal of audiology
pub_type: 杂志文章,随机对照试验
doi:10.1080/14992020500429518
更新日期:2006-03-01 00:00:00
abstract:OBJECTIVE:The purpose of the study was to analyse the role of sound avoidance and anxiety in tinnitus subjects with hyperacusis, defined as hypersensitivity to low to moderate intensity sounds. DESIGN:A group of tinnitus subjects with hyperacusis was compared to tinnitus subjects without hyperacusis, and healthy contr...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.3109/14992027.2012.664290
更新日期:2012-08-01 00:00:00
abstract:OBJECTIVE:To report the prevalence of hearing loss (HL) and associated factors in a nationwide study. DESIGN:Cross-sectional study. STUDY SAMPLE:We investigated the prevalence of HL in 10,845 participants ≥12 years of age and analysed the associated factors with HL from 7434 participants ≥40 years of age. RESULTS:Th...
journal_title:International journal of audiology
pub_type: 杂志文章
doi:10.1080/14992027.2017.1373866
更新日期:2017-12-01 00:00:00