Abstract:
:Lipoprotein lipase deficiency (LLD) is a rare metabolic disorder that typically presents with skin xanthomas and pancreatitis in childhood. We report a case of LLD in an infant who presented with jaundice caused by a pancreatic head mass. Abdominal imaging also incidentally revealed hyperechoic renal masses caused by renal xanthomas. This appearance of the multiple abdominal masses makes this a unique infantile presentation of LLD.
journal_name
Pediatr Radioljournal_title
Pediatric radiologyauthors
Servaes S,Bellah R,Verma R,Pawel Bdoi
10.1007/s00247-010-1560-7subject
Has Abstractpub_date
2010-08-01 00:00:00pages
1440-2issue
8eissn
0301-0449issn
1432-1998journal_volume
40pub_type
杂志文章abstract::This case report describes the incidental finding of intestinal leakage during bone scan imaging with Tc-99m methylene diphosphonate (MDP) in a patient with previously diagnosed protein-losing enteropathy (PLE). Most radiopharmaceuticals reported in the literature that are useful for making this diagnosis are not gene...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-008-0924-8
更新日期:2008-10-01 00:00:00
abstract::We report an 8-month-old girl with portal hypertension secondary to biliary atresia. The decision to treat with TIPS was made at the age of 8 months due to recurrent variceal bleeding. The procedure was carried out with a 6-mm bare stent due to her small size. Radiological follow-up with Doppler US showed gradual sten...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-009-1211-z
更新日期:2009-07-01 00:00:00
abstract::Protocol development between radiology and pediatric emergency medicine requires a multidisciplinary approach to manage straightforward as well as complex and time-sensitive needs for emergency department patients. Imaging evaluation requires coordination of radiologic technologists, radiologists, transporters, nurses...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-008-0973-z
更新日期:2008-11-01 00:00:00
abstract:BACKGROUND:Anteriorly displaced anus is an anomaly that is debated with regard to its nomenclature, diagnosis and management. OBJECTIVE:To describe MRI anatomy of the anal canal in children with anteriorly displaced anus and its impact on the process of defecation. MATERIALS AND METHODS:We prospectively examined ten ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-014-2897-0
更新日期:2014-07-01 00:00:00
abstract::Fetus in fetu is a rare pathological condition, presenting as a congenital tumor. It consists of a malformed parasitic twin that is found within the body of its sibling. Less than 70 cases have been reported and in most of them a definite diagnosis was only made during surgery. We present a case with two fetuses in th...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02012747
更新日期:1994-01-01 00:00:00
abstract::We used the fast field-echo technique of magnetic resonance (MR) imaging with an intravenous bolus injection of paramagnetic contrast agent to evaluate glomerular function. The time-dependent curves of changes in signal intensity observed in the renal cortex and renal medulla brought about by the paramagnetic contrast...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF01395707
更新日期:1996-01-01 00:00:00
abstract:BACKGROUND:Image-guided percutaneous core needle biopsy (PCNB) of soft-tissue lesions is a minimally invasive technique that can provide a definitive diagnosis for treatment. Anatomical and age considerations in children require judicious use of safe percutaneous biopsy techniques. There are, however, limited data on t...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-015-3364-2
更新日期:2015-09-01 00:00:00
abstract:BACKGROUND:The diagnosis of Hirschsprung's disease is usually made in neonates but often considered in older infants and children with constipation: these children may be referred for barium enema. Since it is widely accepted that a normal barium enema does not exclude Hirschsprung's disease, some children, after a nor...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s002470000298
更新日期:2000-10-01 00:00:00
abstract::This article questions the scientific justification of ingrained radiologic practices exemplified by size measurements of childhood solid tumours. This is approached by a critical review of staging systems from a selection of paediatric oncological treatment protocols. Local staging remains size-dependent for some tum...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-014-3148-0
更新日期:2015-01-01 00:00:00
abstract::Primary idiopathic chylopericardium is rare and represents a fraction of all pericardial effusions in the pediatric population. Most cases of chylopericardium occur as a complication of cardiac surgery or after trauma. They may also be caused by tuberculosis, neoplasm, or congenital lymphangiomatosis. Primary idiopath...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-003-0885-x
更新日期:2003-05-01 00:00:00
abstract::Surgical ureteric injury is rare and often unsuspected for a long time. We present a child in whom an abdominal neuroblastoma was completely excised, but during surgery the left ureter was transected and anastomosed. One month later, during postoperative disease staging, abnormal (123)I-MIBG accumulation was observed ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-007-0628-5
更新日期:2008-01-01 00:00:00
abstract:BACKGROUND:Takayasu's arteritis (TA) is a chronic idiopathic inflammatory disease affecting primarily the aorta, its proximal branches and the pulmonary arteries. OBJECTIVES:To retrospectively review the angiograms of children with TA so as to describe the patterns of vascular involvement. PATIENTS AND METHODS:Twenty...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-002-0817-1
更新日期:2003-04-01 00:00:00
abstract::The spectrum of congenital anomalies of the male urethra is presented. The embryologic basis of each anomaly, when known, is discussed. Clinical and imaging features of each entity are presented. ...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-007-0495-0
更新日期:2007-09-01 00:00:00
abstract:BACKGROUND:Whole-body MRI is used for staging paediatric Hodgkin lymphoma, commonly using size thresholds, which fail to detect disease in normal-size lymph nodes. OBJECTIVE:To investigate quantitative whole-body MRI metrics for nodal characterisation. MATERIALS AND METHODS:Thirty-seven children with Hodgkin lymphoma...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-019-04463-9
更新日期:2019-09-01 00:00:00
abstract::58 paediatric patients with pneumonia, in whom an etiological agent had been isolated, were reviewed. The patients were designated to have either viral or bacterial pneumonia on the basis of proposed clinical and radiological criteria. These presumed diagnoses were then compared to the microbiologically proven diagnos...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF00974077
更新日期:1988-01-01 00:00:00
abstract::A 5-year-old girl presented with lower limb deformities, delayed ambulation, short stature, facial dysmorphism and scoliosis. Radiologic examination showed severe anterior and external bowing of the femurs and anterior and internal bowing of the tibia and fibula, with posterior and medial cortical thickening. Square i...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02020841
更新日期:1995-01-01 00:00:00
abstract:BACKGROUND:Knowledge of ovarian volume is important for diagnostic evaluations; however, normal ovarian volume studies on children and adolescents are lacking. OBJECTIVE:This study aimed to analyze age-specific ovarian volume and identify the diverse factors that contribute to ovarian diagnoses. MATERIALS AND METHODS...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-019-04469-3
更新日期:2019-09-01 00:00:00
abstract:BACKGROUND:Dose reduction by combined tube current modulation has not been evaluated in pediatric low-dose CT. OBJECTIVE:This study was performed to evaluate tube current reduction in non-ECG-gated heart CT angiography in children by combined tube current modulation, and to assess the effects of body weight, age, sex,...
journal_title:Pediatric radiology
pub_type: 临床试验,杂志文章
doi:10.1007/s00247-005-0105-y
更新日期:2006-04-01 00:00:00
abstract:BACKGROUND:Pediatric optic pathway gliomas are typically indolent but have a variable clinical course. Treatment is dictated by symptoms and changes on contrast-enhanced MRI examinations. Gadolinium retention in children has motivated parsimonious use of gadolinium-based contrast agents. OBJECTIVES:To determine survei...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-018-4154-4
更新日期:2018-09-01 00:00:00
abstract:BACKGROUND:Magnetic resonance imaging (MRI) T1 relaxometry (mapping) has been reported as a quantitative biomarker of liver injury due to inflammation and fibrosis. OBJECTIVE:To assess the relationship between liver MRI T1 relaxometry measurements obtained using a modified Look-Locker inversion recovery (MOLLI) pulse ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-020-04663-8
更新日期:2020-06-01 00:00:00
abstract:BACKGROUND:While several studies have investigated the dose from scattered radiation from X-ray procedures in a pediatric nursery, they examined scatter from chest procedures only, or the types of examination were not specified. OBJECTIVE:The aim of this study was to collect scatter and transmission data from several ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-003-0999-1
更新日期:2003-10-01 00:00:00
abstract:BACKGROUND:Dual-energy absorptiometry (DXA) is the current reference standard for assessing pediatric osteoporosis; however due to its areal nature, it has limitations. Thus, quantitative ultrasound (QUS), a modality free of ionizing radiation, has been proposed as a potential surrogate for DXA. OBJECTIVE:To semi-quan...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-014-3041-x
更新日期:2014-12-01 00:00:00
abstract::A case of heterotopic gastric mucosa in the common bile duct, cystic duct and gallbladder is reported in a 3-year-old girl with abdominal pain and jaundice. Abdominal US and CT showed dilatation of the biliary tree and a well-defined mass in the common bile duct that narrowed its lumen. The gallbladder was contracted ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-002-0718-3
更新日期:2003-02-01 00:00:00
abstract::Pediatric multiple sclerosis (MS) deserves special attention because of its impact on cognitive function and development. Although knowledge regarding pediatric MS has rapidly increased, understanding the peculiarities of this population remains crucial for disease management. There is limited expertise about the effi...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-019-04582-3
更新日期:2020-05-01 00:00:00
abstract::We present two cases of granulocytic sarcoma of the cervical lymph nodes with central necrosis as an initial manifestation of childhood leukaemia, focusing on the imaging features. Recognition of the CT and MR imaging findings of granulocytic sarcoma involving the cervical lymph nodes assists the differential diagnosi...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-008-0748-6
更新日期:2008-06-01 00:00:00
abstract::Fetal MRI is the modality of choice to study supratentorial brain malformations. To accurately interpret the MRI, the radiologist needs to understand the normal sequence of events that occurs during prenatal brain development; this includes familiarity with the processes of hemispheric cleavage, formation of interhemi...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-020-04696-z
更新日期:2020-12-01 00:00:00
abstract::Historically, the first case of congenital prepyloric membrane in an infant was documented in 1933 [1]. Since then cases have been reported only sporadically in the literature [2-8]. This is a case of congenital antral web which was identified by real-time ultrasonography, confirmed by barium meal study, and proven at...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02016251
更新日期:1992-01-01 00:00:00
abstract::Patients with cat-scratch disease (CSD) may develop visceral manifestations such as hepatic and splenic granulomas. Normally, the granulomas disappear within 1-5 months. Two previous reports have described the evolution of splenic lesions into small calcifications. We report a case of cat-scratch disease in which long...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02012123
更新日期:1994-01-01 00:00:00
abstract:BACKGROUND:Unusual acute symptomatic and reversible early-delayed leukoencephalopathy has been reported to be induced by methotrexate (MTX). OBJECTIVE:We aimed to identify the occurrence of such atypical MTX neurotoxicity in children and document its MR presentation. MATERIALS AND METHODS:We retrospectively reviewed ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-005-0015-z
更新日期:2006-03-01 00:00:00
abstract::Ultrasound (US) has been proposed as an alternative first-line imaging modality to diagnose community-acquired pneumonia in children. Lung US has the potential benefits over chest radiography of being radiation free, subject to fewer regulatory requirements, relatively lower cost and with immediate bedside availabilit...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-017-3910-1
更新日期:2017-10-01 00:00:00