Cardiac liposarcoma and bilateral ovarian mature teratoma in a patient with congenital heart disease and f-anisosplenia.

Abstract:

:A 10-year-old female with atrial septal defect presented with bilateral ovarian mature cystic teratomas. Three spleniculi adjacent to the main spleen were noticed while the endoscopic surgery. Two years later a heart tumor was discovered which led to death. Pathologic examination of samples of the mass proved it to be a liposarcoma. The unusual combination of atrial septal defect, f-anisosplenia (female, congenital heart disease, multiple unevenly-sized spleens, left lung type pulmonary isomerism), bilateral ovarian mature cystic teratomas and liposarcoma of the heart appears to be a unique presentation.

journal_name

Pediatr Blood Cancer

journal_title

Pediatric blood & cancer

authors

Pollono DG,Drut R

doi

10.1002/pbc.21487

subject

Has Abstract

pub_date

2008-08-01 00:00:00

pages

304-5

issue

2

eissn

1545-5009

issn

1545-5017

journal_volume

51

pub_type

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