Abstract:
UNLABELLED:Tracheal bronchus (TB) associated with VACTERL has not been reported previously. A 5-month-old girl with VACTERL association was ventilator-dependent following surgical closure of a patent ductus arteriosus (PDA). Chest radiographs showed persistent hyperinflation of the right upper lobe. Bronchoscopy showed a laterally displaced right main bronchus with stenosis and malacia of the left main bronchus. Dynamic bronchography revealed a TB associated with tracheal stenosis and malacia below the abnormal bronchus. TB may represent an additional tracheal (T) anomaly in VACTERL association. Dynamic bronchography is a useful diagnostic tool in tracheobronchial anomalies. CONCLUSION:TB may represent an "associated" tracheal (T) anomaly in children with VACTERL association. Bronchoscopy may fail to diagnose an ectopic bronchus. Dynamic bronchography is a useful diagnostic tool in tracheobronchial anomalies.
journal_name
Eur J Pediatrjournal_title
European journal of pediatricsauthors
Kairamkonda V,Thorburn K,Sarginson Rdoi
10.1007/s00431-002-1109-3keywords:
subject
Has Abstractpub_date
2003-03-01 00:00:00pages
165-7issue
3eissn
0340-6199issn
1432-1076journal_volume
162pub_type
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