Anaesthetic management of a patient with Emery-Dreifuss muscular dystrophy.

Abstract:

:Emery-Dreifuss muscular dystrophy is a rare form of muscular dystrophy associated with cardiac implications such as cardiomyopathy and arrhythmias leading to sudden death. We describe the anesthetic management of a patient with Emery-Dreifuss muscular dystrophy who presented for orthopaedic surgery and discuss the disorder and its potential anaesthetic implications.

journal_name

Anaesth Intensive Care

authors

Shende D,Agarwal R

doi

10.1177/0310057X0203000320

keywords:

subject

Has Abstract

pub_date

2002-06-01 00:00:00

pages

372-5

issue

3

eissn

0310-057X

issn

1448-0271

pii

2001314

journal_volume

30

pub_type

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