Abstract:
:We present a female patient with T-gamma LGL leukemia, who was followed for the last 20 years. Over these years she developed several autoimmune disorders, including Sjögren's syndrome, Hashimoto's thyroiditis, premature ovarian failure (compatible with type II autoimmune polyglandular syndrome), amegakaryocytic thrombocytopenic purpura, and finally pure red cell aplasia. PCR analysis confirmed rearrangement for TCR gamma. This case emphasizes the complex association of LGL leukemia with autoimmune disorders.
journal_name
Am J Hematoljournal_title
American journal of hematologyauthors
Ergas D,Tsimanis A,Shtalrid M,Duskin C,Berrebi Adoi
10.1002/ajh.10024keywords:
subject
Has Abstractpub_date
2002-02-01 00:00:00pages
132-4issue
2eissn
0361-8609issn
1096-8652pii
10.1002/ajh.10024journal_volume
69pub_type
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