Abstract:
:We describe 10 children with endomyocardial fibrosis who underwent surgical treatment between 1978 and 1999. Seven were male and 3 female, with an age range from 4 to 15 years, having a mean age of 11 years. All were in the final stage of heart failure. Three had biventricular disease, 6 had involvement of the right ventricle alone, and one had endomyocardial fibrosis confined to the left ventricle. There were 3 deaths (30%) in the postoperative period due to low cardiac output. The 7 survivors were followed up for a period ranging from 12 to 168 months, with a mean of 72 months. Two late deaths have occurred resulting from heart failure and infectious endocarditis. Five (50%) children are still alive. Two required 3 reoperations for dysfunction of the inserted valvar prosthesis. One patient is in functional Class IV, and 4 are in Class II to III, despite intensive medical treatment. It is concluded that surgery for endomyocardial fibrosis is an essentially palliative procedure and, especially in children, the results of surgical treatment leave much to be desired.
journal_name
Cardiol Youngjournal_title
Cardiology in the youngauthors
Santos CL,Moraes CR,Santos FL,Moraes F,Brindeiro Filho Ddoi
10.1017/s1047951101000129keywords:
subject
Has Abstractpub_date
2001-03-01 00:00:00pages
205-9issue
2eissn
1047-9511issn
1467-1107journal_volume
11pub_type
杂志文章abstract::Children with a secundum atrial septal defect are usually asymptomatic and are referred for elective closure after 3-4 years of age; however, in premature infants with chronic lung disease, bronchopulmonary dysplasia, or pulmonary hypertension, increased pulmonary blood flow secondary to a left-to-right atrial shunt, ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951114002650
更新日期:2016-01-01 00:00:00
abstract:OBJECTIVE:To evaluate heart rate variability by Holter monitoring in type 1 diabetic children compared with a healthy control group and determine the factors modifying heart rate variability. METHODS:This was designed as a prospective study comparing 28 patients, diagnosed with type 1 diabetes and under follow-up, wit...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951113001224
更新日期:2014-10-01 00:00:00
abstract:INTRODUCTION:Aetiology of protein-losing enteropathy in single-ventricle type CHD is multi-factorial. REPORT:We describe two Fontan patients with protein-losing enteropathy who presented with cytomegalovirus-associated colitis. DISCUSSION:Fontan patients display risk factors for cytomegalovirus-induced gastroenteropa...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120000049
更新日期:2020-03-01 00:00:00
abstract::Sudden cardiac death is a rare but socially devastating event. The most common causes of sudden cardiac death are congenital electrical disorders and structural heart diseases. The majority of these diseases have an incomplete penetrance and variable expression; therefore, patients may be unaware of their illness. In ...
journal_title:Cardiology in the young
pub_type: 杂志文章,评审
doi:10.1017/S1047951112001138
更新日期:2013-04-01 00:00:00
abstract::Prematurity and low birth weight adds to the risk of serious congenital heart disease in infants. It may also delay surgical intervention, especially when cardiopulmonary bypass is required, or where an aortopulmonary shunt is necessary to maintain adequate oxygenation. In this setting, neonatologists are faced with t...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951112000947
更新日期:2013-06-01 00:00:00
abstract::In a neonate born prior to term with a weight of 1825 grams, and diagnosed prenatally as having atrioventricular septal defect and Down's syndrome, we found the aortic arch to be interrupted between the left carotid artery and the left subclavian artery, with the arterial duct being the only route of distal perfusion....
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/s1047951101000622
更新日期:2001-07-01 00:00:00
abstract::A newborn presented with an aorto-right ventricular tunnel, a defect connecting the left aortic sinus to the right ventricle. The patient underwent repair on 4th day of life. ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951115001572
更新日期:2016-01-01 00:00:00
abstract::Innocent murmurs are common in childhood. They require accurate diagnosis to avoid unnecessary anxiety and/or restrictions. With this in mind, we studied prospectively children diagnosed by a paediatric cardiologist as having innocent murmurs to review the necessity of investigations in excluding organic abnormalities...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/s104795110000963x
更新日期:2000-10-01 00:00:00
abstract::The arterial switch operation has become the preferred procedure for surgical management of transposition, defined on the basis of concordant atrioventricular and discordant ventriculo-arterial connections. We conducted a retrospective evaluation of our experience in 61 infants with this segmental combination, seen fr...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951107001746
更新日期:2008-02-01 00:00:00
abstract:OBJECTIVE:We aimed to apply systems engineering principles to address hospital-acquired infections in the paediatric intensive care setting. DESIGN:Mixed method approach involving four steps: perform time-motion study of cardiac intensive care unit (CICU) care processes, establish a meaningful schema to classify obser...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120003777
更新日期:2020-11-10 00:00:00
abstract:OBJECTIVE:The aim of this study was to investigate the relations between the P-wave dispersion and diastolic functions in type 1 diabetic children. PATIENTS:A total of 33 diabetic patients without any cardiovascular disease, with a mean age of 12.3 plus or minus 4.2 years, and 29 healthy controls, with a mean age of 1...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S104795110999031X
更新日期:2010-04-01 00:00:00
abstract::Acute myocardial infarction is rarely reported in children. Most of the cases are secondary to congenital anomalies or Kawasaki disease. Coronary artery total occlusion caused by fibromuscular dysplasia has never been reported in young children. Here we report a case of a 12-year-old boy with fibromuscular dysplasia, ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951113002394
更新日期:2015-01-01 00:00:00
abstract:BACKGROUND:Absent arterial valve leaflets are rare anomalies. On the basis of our understanding of the normal development of the arterial valves, we draw inferences that might offer clues to their morphogenesis. METHODS:We describe the findings from four human fetal autopsies with so-called "absent" arterial valvar le...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951116000524
更新日期:2017-03-01 00:00:00
abstract::The persistence of so-called spongy myocardium was first reported in humans in the 1960s. Subsequently, a few reports described the condition, utilizing inconsistent facts and terminology. In 1990 the first report appeared using the term "noncompaction", and detailed its clinical implications. Following this report, m...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951108001972
更新日期:2008-06-01 00:00:00
abstract:OBJECTIVE:To categorise records according to primary cardiac diagnosis in the United Kingdom Central Cardiac Audit Database in order to add this information to a risk adjustment model for paediatric cardiac surgery. DESIGN:Codes from the International Paediatric Congenital Cardiac Code were mapped to recognisable prim...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951112001369
更新日期:2013-08-01 00:00:00
abstract::We describe a case of transcatheter occlusion of a large and tortuose coronary artery fistula in an 8-year-old girl. During 2.5 years' of follow-up, she had no complaints and developed normally. This method of reserving the guide wire in cardiac catheterisation is extremely useful. Through the application of a patent ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S104795111000137X
更新日期:2011-02-01 00:00:00
abstract:BACKGROUND:Transcatheter closure of atrial septal defects is performed under fluoroscopy, but echocardiography has gained an important role in the procedure. With the new Amplatzer Septal Occluder a device has become available which is easy to implant with minimal fluoroscopy time. We developed an interventional proced...
journal_title:Cardiology in the young
pub_type: 临床试验,杂志文章
doi:10.1017/s1047951100008349
更新日期:1999-03-01 00:00:00
abstract::IntroductionChildren with CHD and acquired heart disease have unique, high-risk physiology. They may have a higher risk of adverse tracheal-intubation-associated events, as compared with children with non-cardiac disease.Materials and methodsWe sought to evaluate the occurrence of adverse tracheal-intubation-associate...
journal_title:Cardiology in the young
pub_type: 杂志文章,多中心研究
doi:10.1017/S1047951118000495
更新日期:2018-07-01 00:00:00
abstract:OBJECTIVE:To examine the current subjective state of health, and the longitudinal course of psychological well-being, in adult patients with congenital cardiac malformations. METHODS:Our study concerns the second follow-up of a cohort of patients with congenital cardiac malformations. We examined 362 consecutive patie...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951105000351
更新日期:2005-04-01 00:00:00
abstract::The purpose of our paper is to assess the prognostic value of balloon occlusion as a test for patients with various types of functionally single ventricle after different palliative surgical procedures who were candidates for further modifications of a cavo-pulmonary operation. In all patients, there were at least two...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:
更新日期:2003-08-01 00:00:00
abstract::Myocarditis is an important cause of arrhythmogenic sudden cardiac arrest in the young. A strong index of suspicion is required as not only can arrhythmias be the only clinical manifestation but also because these patients can have normal cardiac biomarkers, electrocardiographic and echocardiographic findings, and inf...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120001523
更新日期:2020-08-01 00:00:00
abstract::A 5-week-old child presented with a cardiac arrest secondary to myocardial ischaemia. Echocardiography demonstrated a single coronary artery arising from the right sinus of Valsalva. The coronary artery branched into left and right arteries, with the left artery then coursing anomalously in the tissue plane between th...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951104006092
更新日期:2004-12-01 00:00:00
abstract:BACKGROUND:Complete transposition is the most common form of neonatal cyanotic heart disease. The management of this condition has changed markedly in the last decade and there appears to be a significant variation between centres in terms of pre-operative management. OBJECTIVES/METHODS:We surveyed all paediatric card...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/s104795110000812x
更新日期:2000-09-01 00:00:00
abstract:INTRODUCTION:Although chylothorax is an uncommon complication following paediatric cardiothoracic surgery, it has significant associated morbidities and increased in-hospital mortality, as well as results in higher costs. A lack of prospective evidence or consensus guidelines for management of chylothorax further hinde...
journal_title:Cardiology in the young
pub_type: 杂志文章,多中心研究
doi:10.1017/S1047951119001525
更新日期:2019-09-01 00:00:00
abstract::We report a case of Uhl's anomaly in a 5-month-old cyanotic infant who presented with thromboembolic stroke and acute hemiparesis. The patient underwent successfully an initial surgical repair, which included exclusion of the right ventricle by patch closure of the tricuspid valve, atrial septectomy and construction o...
journal_title:Cardiology in the young
pub_type: 杂志文章,评审
doi:10.1017/s1047951102000410
更新日期:2002-03-01 00:00:00
abstract:OBJECTIVES:To assess clinical presentation, treatment, and outcome of children with Ebstein's anomaly. BACKGROUND:Data on long-term outcome of children with Ebstein's anomaly are scarce. METHODS:Retrospective analysis of all children with Ebstein's anomaly treated between February, 1979 and January, 2009 in a single ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951112000224
更新日期:2013-02-01 00:00:00
abstract::With the advent of improved medical and surgical care in congenital heart disease, there has been an increase in the number of patients who survive into adulthood, giving rise to a new patient population 'Adults with congenital heart disease'. In the past, morbidity and mortality were the primary concerns for this gro...
journal_title:Cardiology in the young
pub_type: 杂志文章,评审
doi:10.1017/S1047951113000747
更新日期:2014-02-01 00:00:00
abstract::Critical heart disease in the pediatric population is associated with high morbidity and mortality. Research around the most effective communication and decision-making strategies is lacking. This systematic review aims to summarise what is known about parent preference for communication and decision-making in childre...
journal_title:Cardiology in the young
pub_type: 杂志文章,meta分析,评审
doi:10.1017/S1047951118001233
更新日期:2018-10-01 00:00:00
abstract:INTRODUCTION:The term cor triatriatum is used to describe a fibromuscular partition that divides an atrium into two compartments. It was first used by Borst in 1905, although the lesion had been described before by Church in 1868. Both described divided left atrial chamber (also referred to as cor triatriatum sinister)...
journal_title:Cardiology in the young
pub_type: 杂志文章,评审
doi:10.1017/S1047951114001073
更新日期:2015-02-01 00:00:00
abstract:BACKGROUND:In patients with tricuspid atresia palliated by construction of a total cavopulmonary connection, both pulmonary and systemic circulations depend on the performance of the dominant left ventricle. When estimating the volume of such ventricles using cross-sectional echocardiography, it is necessary to make as...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/s1047951100006521
更新日期:2000-03-01 00:00:00