Endomyocardial fibrosis in children.

Abstract:

:We describe 10 children with endomyocardial fibrosis who underwent surgical treatment between 1978 and 1999. Seven were male and 3 female, with an age range from 4 to 15 years, having a mean age of 11 years. All were in the final stage of heart failure. Three had biventricular disease, 6 had involvement of the right ventricle alone, and one had endomyocardial fibrosis confined to the left ventricle. There were 3 deaths (30%) in the postoperative period due to low cardiac output. The 7 survivors were followed up for a period ranging from 12 to 168 months, with a mean of 72 months. Two late deaths have occurred resulting from heart failure and infectious endocarditis. Five (50%) children are still alive. Two required 3 reoperations for dysfunction of the inserted valvar prosthesis. One patient is in functional Class IV, and 4 are in Class II to III, despite intensive medical treatment. It is concluded that surgery for endomyocardial fibrosis is an essentially palliative procedure and, especially in children, the results of surgical treatment leave much to be desired.

journal_name

Cardiol Young

journal_title

Cardiology in the young

authors

Santos CL,Moraes CR,Santos FL,Moraes F,Brindeiro Filho D

doi

10.1017/s1047951101000129

keywords:

subject

Has Abstract

pub_date

2001-03-01 00:00:00

pages

205-9

issue

2

eissn

1047-9511

issn

1467-1107

journal_volume

11

pub_type

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