Abstract:
OBJECTIVE:Fibrogenesis imperfecta ossium is an extremely rare disorder that can easily be misdiagnosed. We retrospectively reviewed the clinical and imaging data of three confirmed cases of fibrogenesis imperfecta. DESIGN AND PATIENTS:The patients consisted of two men and one woman, ranging in age from 40 to 53 years. Radiography was performed in all the patients. One patient had a 3-year follow-up of the thoracolumbar spine with conventional radiography and thoracolumbar magnetic resonance (MR) imaging. Open biopsy was performed in all cases, confirming the diagnosis of fibrogenesis imperfecta ossium. RESULTS:All our cases demonstrated "fishnet" trabecular pattern by conventional radiographs, and a pelvis radiograph of one patient showed an equivocal sclerosis pattern. Multiple fractures were noted in two patients. A pseudoexostosis was present in the ilium in one patient. Thoracolumbar MR imaging demonstrated diffuse low signal intensity within the medullary space on both T1-weighed and T2-weighted images, except for a region of increased signal intensity in the L1 and L2 vertebral bodies on T2-weighed images due to edema from acute collapse. CONCLUSIONS:Although uncommon, fibrogenesis imperfecta ossium should be considered in a previously healthy patient with a combination of progressive bone pain, unexplained fractures, a radiologic pattern of fishnet osteopenia and MR imaging of low signal intensity bone marrow on both T1-weighted and T2-weighted images.
journal_name
Skeletal Radioljournal_title
Skeletal radiologyauthors
Wang CS,Steinbach LS,Campbell JB,Hayashi G,Yoon ST,Johnston JOdoi
10.1007/s002560050535keywords:
subject
Has Abstractpub_date
1999-07-01 00:00:00pages
390-5issue
7eissn
0364-2348issn
1432-2161journal_volume
28pub_type
杂志文章abstract::A case of sclerosing epithelioid fibrosarcoma and its appearance on MRI is presented. The tumor showed a zonal architecture on MRI with a large central core of very low signal intensity and a peripheral rim of intermediate to high signal intensity on T1- and T2-weighted spin echo pulse sequences. The core showed decre...
journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/s002560050297
更新日期:1997-10-01 00:00:00
abstract::We report on a case of a deforming arthropathy in a young man with a lysosomal storage disorder. A 31-year-old man with a known diagnosis of mannosidosis presented with a painful swollen right elbow. Radiographs of his right elbow showed a disorganised joint with multiple fragments resembling the appearances of a neur...
journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/s002560000213
更新日期:2000-06-01 00:00:00
abstract:OBJECTIVE:The transverse relaxation time (T2) in MR imaging has been identified as a potential biomarker of hyaline cartilage pathology. This study investigates whether MR assessments of T2 are comparable between 3-T scanners from three different vendors. DESIGN:Twelve subjects with symptoms of knee osteoarthritis and...
journal_title:Skeletal radiology
pub_type: 杂志文章,多中心研究
doi:10.1007/s00256-012-1511-5
更新日期:2013-04-01 00:00:00
abstract:OBJECTIVE:To assess dynamic contrast-enhanced magnetic resonance imaging (DCE MRI) as a measure of vascularity in scaphoid delayed-union or non-union. MATERIALS AND METHODS:Thirty-five patients (34 male, one female; mean age, 27.4 ± 9.4 years; range, 16-51 years) with scaphoid delayed-union and non-union who underwent...
journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/s00256-013-1627-2
更新日期:2013-07-01 00:00:00
abstract::We report on a rare case of an intraosseous hemangioma involving the proximal tibia in a 70-year-old man. Radiographically, the lesion was a well-defined osteolytic lesion with marginal sclerosis. The CT images demonstrated a well-defined osteolytic lesion with partial cortical breakthrough. T1-weighted MR images show...
journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/s002560000256
更新日期:2000-09-01 00:00:00
abstract::A broken needle is a rare complication of bone biopsy. We describe an easily applied technique of retrieval of a retained biopsy needle fragment using a cannulated drill typically used for internal fixation of femoral neck fractures. This approach allows for removal under moderate conscious sedation and can be perform...
journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/s00256-019-03304-y
更新日期:2020-02-01 00:00:00
abstract::The appearance on magnetic resonance imaging (MRI) of 16 cases of pathologically proven eosinophilic granuloma were reviewed retrospectively and correlated with the radiographic appearance of the lesion. The most common MR appearance (ten cases) was a focal lesion, surrounded by an extensive, ill-defined bone marrow a...
journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/BF00206144
更新日期:1993-01-01 00:00:00
abstract:OBJECTIVE:To investigate the MR findings of necrotic lesions and the extralesional area of osteonecrosis of the femoral head (ONFH) for each of the radiological stages. DESIGN AND PATIENTS:Forty-nine hips in 29 patients (15 female, 14 male; mean age 38 years, range 17-59 years) were imaged using a 1.0-T superconductin...
journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/s002560050583
更新日期:2000-03-01 00:00:00
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journal_title:Skeletal radiology
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doi:10.1007/s002560050363
更新日期:1998-04-01 00:00:00
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journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/s00256-007-0285-7
更新日期:2007-08-01 00:00:00
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journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/s00256-015-2290-6
更新日期:2016-02-01 00:00:00
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journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/s002560000284
更新日期:2000-12-01 00:00:00
abstract:PURPOSE:To evaluate the prevalence, imaging appearance, and significance of popliteal lymph nodes (PLN) on magnetic resonance imaging (MRI) in patients with distal femoral or proximal tibial osteosarcoma (OS). METHOD AND MATERIALS:This study included consecutive patients with OS presenting from May 2016 to March 2018....
journal_title:Skeletal radiology
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更新日期:2020-11-01 00:00:00
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journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/s00256-015-2173-x
更新日期:2015-09-01 00:00:00
abstract::Shoulder girdle lipomatosis is a distinct type of lipomatosis which has unique clinical and radiographic features. The MR findings reflect the pathologic findings and, in our opinion, allow the differentiation of shoulder girdle lipomatosis from other lipomatous masses on the basis of imaging findings alone. ...
journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/BF00941252
更新日期:1995-08-01 00:00:00
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journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/BF00361052
更新日期:1986-01-01 00:00:00
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journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/s00256-014-1918-2
更新日期:2014-10-01 00:00:00
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journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/s00256-007-0423-2
更新日期:2008-03-01 00:00:00
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journal_title:Skeletal radiology
pub_type: 杂志文章,评审
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更新日期:2012-11-01 00:00:00
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journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/s002560050486
更新日期:1999-02-01 00:00:00
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journal_title:Skeletal radiology
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journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/s00256-010-1037-7
更新日期:2011-05-01 00:00:00
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journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/BF01106096
更新日期:1991-01-01 00:00:00
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journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/BF00367381
更新日期:1982-01-01 00:00:00
abstract::A 2-year-old child presenting with bone pain and bone lesions was found to have sinus histiocytosis with massive lymphadenopathy (SHML). SHML presenting with skeletal symptoms is unusual. Management has been conservative and the child has been symptom free for 30 months, although the bone lesions have not completely r...
journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/s002560050349
更新日期:1998-02-01 00:00:00
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journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/s00256-019-3159-x
更新日期:2019-08-01 00:00:00
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journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/BF00347373
更新日期:1981-01-01 00:00:00
abstract::We evaluated the relative contribution of plain radiographs and computed tomography to the assessment of fracture healing under experimental circumstances. In 15 sheep, we performed midshaft femoral osteotomies and internal fixation of the resultant segmental fractures. Radiographs were obtained preoperatively and imm...
journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/BF00355070
更新日期:1986-01-01 00:00:00
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journal_title:Skeletal radiology
pub_type: 杂志文章
doi:10.1007/s00256-011-1197-0
更新日期:2012-05-01 00:00:00